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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Human
Satellite cell
Inflammation
Calcium
Dysferlin
AAV
Muscle dystrophy
Myogenesis
PABPN1
Haploinsufficiency
Anti-fibrotic pharmacotherapies
Myopathies
Accelerometry
Gene therapy
Intercellular communication
Duchenne muscular dystrophy
Bioinformatique
Gene replacement
CNOT6L
APOPTOSIS
Nuclear envelope
Muscle
C2 domains
Adipose tissue
Actin
Aggregate
PABPN1 agregates
DUX4
Myotube
Aav-U7
Autologous
ALS
Anti-acetylcholine receptor antibodies
Myoblasts
Bile salt hydrolases
Antisens oligonucleotides
Alzheimer's disease
Arbovirus
Myosin
2-D PAGE
Antiserum
CS
Thérapie génique
Myositis
Muscle stem cells
RNA
C2C12 cells
ARN
Neuromuscular junction NMJ
Transcriptomics
Alphavirus
Sarcopenia
Andermann syndrome
GENE
Akt
Myopathy
Differentiation
Muscle strength
Xenograft
Biopsies humaines
DMD
DNA methylation
Bioinformatics
Dystrophin
Agrégats de PABPN1
Cross-bridge kinetics
Oculopharyngeal muscular dystrophy
Botulinum neurotoxin
Pharyngeal muscle
Satellite cells
OPMD
AAV vectors
Lamins
CD49d
FSHD
Triplet expansion disease
Functional genomics
Fibrosis
Ageing
Muscle fibrosis
Annexin A2
AChR antibodies
Biomarker
Exon-skipping
MUTATIONS
Myoblast
Dysferlinopathy
Regeneration
Cell therapy
BINDING SPECIFICITY
Skeletal muscle
Pax7
Autoimmune diseases
Metabolism
Dystrophie musculaire oculopharyngée
FAPs
AUTOPHAGY
Atrophy
Geriatric assessment
Aged